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Evidence-Based Practice Recommendations for Nutrition-Related Management of Children and Adults with Cystic Fibrosis and Pancreatic Insufficiency: Results of a Systematic Review

      Abstract

      The Cystic Fibrosis Foundation established a process of systematic review of evidence to inform the development of clinical care guidelines and encourage evidence-based practice. The Subcommittee on Growth and Nutrition reviewed the evidence in two areas: energy intake and dosing for pancreatic enzyme replacement therapy. Evidence-based recommendations are presented here. Also, an ad hoc working group conducted a review of the literature and performed new analyses using the Cystic Fibrosis Foundation Patient Registry to update the recommendations for growth and weight-status monitoring. These Registry data–based recommendations are presented.
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      Biography

      V. A. Stallings is director, Nutrition Center, and director, Office of Faculty Affairs, Division of Gastroenterology, Hepatology, and Nutrition, The Children's Hospital of Philadelphia, Philadelphia, PA.

      Biography

      L. J. Stark is professor of pediatrics and director, Division of Behavioral Medicine and Clinical Psychology, Children's Hospital Medical Center, University of Cincinnati College of Medicine, Cincinnati, OH.

      Biography

      K. A. Robinson is co-director, Johns Hopkins Evidence-based Practice Center, and research associate, Division of Internal Medicine, Johns Hopkins University School of Medicine, Baltimore, MD.

      Biography

      A. P. Feranchak is assistant professor pediatrics, Pediatric Gastroenterology, Hepatology, and Nutrition, University of Texas Southwestern Medical Center at Dallas.

      Biography

      H. Quinton is with the Dartmouth Hitchcock Medical Center, Lebanon, NH.

      Linked Article

      • Dietetic Management of People with Cystic Fibrosis
        Journal of the American Dietetic AssociationVol. 108Issue 12
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          We read with interest the report by Stallings and colleagues on the recommendations of the US Cystic Fibrosis Foundation's Subcommittee on Growth and Nutrition (1). This guidance will assist dietetic management of people with cystic fibrosis, particularly with regard to identifying those at nutritional risk.
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